Mad Cows or Mad Scientists? The world is going mad over mad cow disease. Hundreds of thousands of cows have been slaughtered. Beefeaters live in fear of developing similar brain degeneration, known in humans as Creutzfeldt Jakob disease (CJD.
Prions: Infectious Proteins It was not until the work of American scientist Stanley B. Prusiner was recognized with the Nobel Prize in Physiology in 1997 that we began to understand how prions act as agents in mad cow disease.